PRENATAL DIAGNOSIS OF ECTOPIA CORDIS. Case Report

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Vol. 86 No. 2 (2008): Issue Feb 2008

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Dalenda Chelli
Service A de gynécologie obstétrique
Kaouther Dimassi
Service A de gynécologie obstétrique
Souhir Jallouli-Bouzguenda
Service de foetopathologie
Essia Ebdellah
Service A de gynécologie obstétrique
Feten Hermi
Centre de maternité et de néonatologie la Rabta Tunis.
Bechir Zouaoui
Service A de gynécologie obstétrique
Ezzeddine Sfar
Service A de gynécologie obstétrique
Tania Kitova
Service de foetopathologie
Hela Chelli
Service A de gynécologie obstétrique
Mohamed Badis Channoufi
Service A de gynécologie obstétrique
Soumaya Gaigi
Service de foetopathologie

Abstract

Ectopia cordis is a rare and impressive malformation presenting as an isolated lesion or as part of the Cantrell’s pentology syndrom. It is defined as an anomaly in which the fetal heart lies outside the thoracic cavity.
The aim of the study is to report the prenatal diagnostic features and management of ectopia cordis.
Case report : We report a prenatal diagnosis case of ectopia cordis using two-dimensional ultrasound at 19 weeks of gestation. Multiple congenital anomalies were found. The most important one was the presence of a ventral thoracoabdominal wall defect with exstrophy of the heart, liver, stomach and intestines. Histopathological examination confirmed the ultrasound findings. Due to severity of the malformations, termination of pregnancy was made.

Keywords:

Ectopia cordis, ultrasonography, Extrathoracic heart, prenatal diagnosis

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