What prognosis for Ebstein's anomaly without surgery? Hassan II teaching hospital experience.

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Published Sep 6, 2016
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Vol. 94 No. 4 (2016): Issue Apr 2016

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Moumouni Garba
Samir Atmani
Rabiou Sani
Kaled Adamou Nouhou

Abstract

Abstract:

Background: From the first description in 1886, significant progress was made on the treatment of Ebstein disease by mono and bi-ventricular surgery.
Aim: To highlight the prognosis of Ebstein's anomaly in the pediatric department of Hassan II hospital in Fez.
Methods: This is a descriptive and retrospective study of 4 years.
Results: We collected nine patients (seven boys and two girls) with a mean age of 5.3 years. Cyanosis was the main mode of revelation of the disease. In three patients Ebstein's anomaly was part of a malformative syndrome. All patients had only symptomatic medical treatment. Five patients are still alive at a follow up of one to six years.
Conclusion: Symptomatic medical treatment of Ebstein malformation may improve the prognosis of the disease.

Keywords:

Key words: Ebstein anomaly, prognosis, management

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